Differences in Protein Quality Control Correlate with Phenotype Variability in 2 Mouse Models of Familial Amyotrophic Lateral Sclerosis
NEUROBIOLOGY OF AGING(2015)
关键词
ALS,SOD1G93A transgenic mouse,Protein quality control,Chaperone,Alpha-B-crystallin,Cyclophillin-A,Proteasome,Autophagy
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